Pathways of ammonia detoxification to GLN in muscles linked to Improved usage on the BCAA and ?-KG (cataplerosis) and advised consequences of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Constructive outcome of BCAA on ammonia detoxification to GLN could be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylbu